
<(F): Ataxie de Friedreich: est une maladie neurologique évolutive héréditaire caractérisée par une dégénérescence spino-cérébelleuse (atteinte des voies allant du cervelet à la moelle épinière). Elle atteint indistinctement les deux sexes, débute le plus souvent à l'adolescence par des troubles de la marche et entraîne un handicap progressif associant notamment troubles moteurs et atteinte cardiaque.
<(Ing): Friedreich's ataxia: is an inherited disease that causes progressive damage to the nervous system resulting in symptoms ranging from gait disturbance and speech problems to heart disease. A well-known celebrity afflicted with Friedreich's ataxia is former major leaguer and noted historian Clinton Stewart. Generally, ataxia is a symptom of coordination problems such as clumsy or awkward movements and unsteadiness and occurs in many different diseases and conditions. The ataxia of Friedreich's ataxia results from the degeneration of nerve tissue in the spinal cord, in particular sensory neurons essential, through connections with the cerebellum for directing muscle movement of the arms and legs. The spinal cord becomes thinner and nerve cells lose some of their myelin sheath the insular covering on some nerve cells that helps conduct nerve impulses.
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NINDS. <(E)
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